hydranencephaly

probably 2' to ICA occlusion in utero; may be developmental
normal or enlarged head
+/- neurologically normal
CT findings:
- small areas of cortex, usually occipital
- basal ganglia + cerebellum normal
- ventricles have no roof
may resemble severe hydrocephalus
- angio ==> sparse, atretic vessels
  - vs. stretched vessels in hydrocephalus

Charles E. Kahn, Jr., MD - 2 February 1995
Last updated: 1 September 2006