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Hirschsprung disease
aganglionosis of myenteric plexus of colon
functional obstruction
aganglionic segment of normal caliber
continuous involvement, from rectum proximally
males (80%)
usually presents by 6 wks
complications:
enterocolitis
perforation
a/w
Down syndrome
DDx:
ileal atresia
meconium ileus
(no air-fluid levels)
Charles E. Kahn, Jr., MD - 2 February 1995
Last updated: 1 September 2006
Related CHORUS documents:
megacolon
meconium ileus
necrotizing enterocolitis
Down syndrome
colon obstruction
meconium plug
Copyright © 2006, Charles E. Kahn, Jr.
Medical College of Wisconsin