bullous diseases of esophagus

• epidermolysis bullosa dystrophica
  • autosomal recessive
  • presents in infancy or later life
  • epidermal-dermal separation
  • +/- anal strictures
  • Rx: conservative, soft diet

• benign mucous membrane (cicatricial) pemphigoid
  • not "pemphigus vulgaris"
  • not bullous pemphigoid
  • females (2:1), elderly

© 2002, C.E. Kahn, Jr.
2002-04-18