cystic fibrosis

probably autosomal recessive
common in whites, 1:2000
clinically: resp. disease, GI symptoms

complications:

bronchiectasis
pneumothorax
hemoptysis
lobar atelectasis
pulmonary HTN
cor pulmonale {normal-size heart may represent CMG}
large, opacified sinuses

DDx: Riley-Day syndrome

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© 2002, C.E. Kahn, Jr.
2002-04-18