pheochromocytoma

• "10-percent rule"
  • 10% bilateral
  • 10% malignant
  • 10% extra-adrenal

• associated syndromes:
  • neurofibromatosis
  • von Hippel-Lindau
  • multiple endrocine neoplasia: MEN-2 and MEN-3

• extra-adrenal sites:
  • detected with MIBG
  • includes organ of Zuckerkandl(most common)

© 2002, C.E. Kahn, Jr.
2002-04-18