Potter syndrome

I

autosomal recessive ("infantile") polycystic disease

• "microscopic" (1-mm) cysts
• US: +/- increased echo, no gross cysts

II

multicystic dysplastic kidney ("renal dysplasia")

• US: multiple cysts, usually unilateral

III

autosomal dominant ("adult") polycystic disease

• usually not present until adult life
• US: multiple cysts

renal agenesis

associated with:

• oligohydramnios
• abnormal facies
• hypoplastic lungs

© 2002, C.E. Kahn, Jr.
2002-04-18