white-matter disease
- destruction of existing myelin
- acquired diseases with inflammatory characteristics
- includes: MS, PML, encephalomyelitis
- also may be d/t anoxia, infarct, tumor, radiation
- abnormal myelin formation or maintenance
- two groups:
- primary white-matter diseases: leukodystrophies
- involve gray matter: Niemann-Pick, Gaucher,
Tay-Sachs
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© 2002, C.E. Kahn, Jr.
2002-04-18