liver hemangioendothelioma

• females (67%)
• infants (90% before 6 m/o)

• sx: mass (hepatomegaly)
• cutaneous hemangiomas (45%)
• mildly increased aFP (occasionally)
• +/- CHF 2' to shunting (only 4%)

• usually diffuse, precludes surgery
• most involute spontaneously or with steroids

  DDx:

  • mesenchymal hamartoma
  • cavernous hemangioma
  • hepatoma
  • hepatoblastoma (increased aFP)
  • metastatic neuroblastoma (increased serum VMA)

© 2002, C.E. Kahn, Jr.
2002-04-18