asplenia / polysplenia syndromes

probably different degrees of the same disorder

asplenia (Ivemark syndrome, bilateral right sidedness)
- more severe
- right lung lobar anatomy bilaterally, bilateral eparterial bronchi
- associated with cardiac, GI/GU and situs anomalies
  - TAPVR(~100%),ECD(85%)and many others
- Howell-Jolly bodies - RBC inclusions
polysplenia (bilateral left-sidedness)
- left lung lobar anatomy bilaterally, bilateral hyparterial bronchi
- multiple spleens/splenules
- bilateral SVCs, azygos continuation of IVC
- associated with cardiac(less common than in asplenia), GI/GU and situs anomalies