lymphangioleiomyomatosis (LAM)
- females
- chylous pleural effusions
- interstitial infiltrate at bases (d/t smooth muscle proliferation)
- post-obstructive emphysema
- +/- spontaneous pneumothorax
(DDx: eosinophilic granuloma)
- similar appearance of tuberous sclerosis
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© 2002, C.E. Kahn, Jr.
2002-04-18