Hirschsprung disease

• aganglionosis of myenteric plexus of colon
  • functional obstruction
  • aganglionic segment of normal caliber
  • continuous involvement, from rectum proximally

• males (80%)
• usually presents by 6 wks

• complications:
  • enterocolitis
  • perforation

• a/w Down syndrome

• ileal atresia
• meconium ileus (no air-fluid levels)

© 2002, C.E. Kahn, Jr.
2002-04-18