portal hypertension: classification

• extrahepatic:
  • portal vein obstruction (extrinsic compression, phlebitis, OC, coagulopathy, tumor invasion, pancreatitis, neonatal omphalitis)
  • dynamic: traumatic/neoplastic arterioportal fistula
  • segmental portal HTN: splenic/SMV occlusion
• intrahepatic (obstruction of portal venules):
  • congenital hepatic fibrosis
  • primary biliary cirrhosis
  • sarcoid
  • myelofibrosis
  • schistosomiasis
  • idiopathic noncirrhotic fibrosis
  • Wilson disease
  • reticuloendotheliosis
  • Felty syndrome
  • chronic malaria
  • toxic fibrosis (arsenic, copper, PVC vapors)

• cirrhosis
• sclerosing cholangitis

• Budd-Chiari syndrome
• constrictive pericarditis
• congestive heart failure

© 2002, C.E. Kahn, Jr.
2002-04-18