nephroblastomatosis

persistent primitive renal tissue (normally present up to 36 weeks)

potential precursor to Wilms tumor: present in 30% of kidneys with single and 100% of kidneys with bilateral Wilms tumor

associated with:

hemihypertrophy
sporadic aniridia
pseudohermaphroditism
Klippel-Trenaunay syndrome
Beckwith-Wiedemann syndrome
splenic agenesis with hepatic malformation

findings:

kidneys may be enlarged
deformity of the pelvocalyceal system
US: subtle subcapsular nodules (hypo-/iso-/hyperechoic)
CT: hypodense subcapsular nodules after contrast enhancement

[Home] [Kidney] [Disclaimer]

© 2002, C.E. Kahn, Jr.
2002-04-18