tetralogy of Fallot

underdevelopment of pulmonary infundibulum

8% of all congenital heart disease
most common CHD with cyanosis after 1 year of life

TETRAD:

obstruction of RV outflow tract; usually at the pulmonary infundibulum, occasionally at pulmonary valve
VSD
RV hypertrophy
aorta overriding the interventricular septum

associated with:

bicuspid pulmonary valve (40%)
stenosis of left pulmonary artery (40%)
right-sided aortic arch (25%)
TE fistula
Down syndrome
anomalies of coronary arteries (10%)
forked ribs, scoliosis

see congenital heart disease

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© 2002, C.E. Kahn, Jr.
2002-04-18