Mounier-Kuhn syndrome
tracheomegaly, tracheobronchomegaly
- inheritance: (?) autosomal recessive
clinical findings:
XR findings:
- tracheobronchomegaly (trachea equal to or greater
than the width of the tracheal vert. body.
- increase in lumen of the trachea with Valsalva
and narrowing with Muller maneuver.
- saclike recesses
- pulmonary fibrosis
- bullae
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© 2002, C.E. Kahn, Jr.
2002-04-18