Muir-Torre syndrome
- rare syndrome consisting of:
- soft tissue tumors: keratoacanthoma, actinic keratosis, etc.
- internal malignancies (50% gastrointestinal, 25% genito-urinary)
- autosomal dominant inheritance
- high incidence of colonic polyps
- 120 reported cases
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© 2002, C.E. Kahn, Jr.
2002-04-18